- Protoporphyrin Retention in Hepatocytes and Kupffer Cells Prevents Sclerosing Cholangitis in Erythropoietic Protoporphyria Mouse Model
[作者:Lyoumi, S; Abitbol, M; Rainteau, D; Karim, Z; Bernex, F; Oustric, V; Millot, S; Letteron, P; Heming, N; Guillmot, L; Montagutelli, X; Berdeaux, G; Gouya, L; Poupon, R; Deybach, JC; Beaumont, C; Puy, H,期刊:Gastroenterology, 页码:1509-U533 , 文章类型: Article,,卷期:2011年141-4]
- BACKGROUND & AIMS: Chronic, progressive hepatobiliary disease is the most severe complication of erythropoietic protoporphyria (EPP) and can require liver transplantation, although the mechanisms that lead to liver failu...
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